Hyperinsulinaemia, resulting from islet cell hyperplasia, is a common early complication. The associated hypoglycaemia may be controlled with steroids or glucagon. Rarely, subtotal pancreatectomy may be necessary.
In the long term, this syndrome is associated with an increased incidence of solid tumours such as nephroblastoma and hepatoblastoma. The incidence of these are increased if there is hemihypertrophy.
Add information to this page that would be handy to have on hand during a consultation, such as a web address or phone number. This information will always be displayed when you visit this page