This site is intended for healthcare professionals

Sign in
Go to /sign-in page

You can view 5 more pages before signing in

Management

Last reviewed dd mmm yyyy. Last edited dd mmm yyyy

Authoring team

Treatment is essentially symptomatic. Hands and feet should be kept warm and regular chiropody offered. Any infection, dysphagia or hypertension should be treated. Different treatment regimes have been used in the management of this disease:

  • ACE inhibitors - management and prevention of renal failure
  • penicillamine - has been used in an attempt to halt the fibrotic process
  • systemic steroids combined with cyclophosphamide - has been used in the management of respiratory disease
  • H2 blockers / proton pump inhibitors for symptoms of reflux

Raynaud's phenomenon may be successfully managed.

The disease may be mild or severe. The mean 5-year survival is about 70% in the absence of renal disease. Increasing levels of plasma renin may herald rapid deterioration.

Related pages

Create an account to add page annotations

Create a free account

Add information to this page that would be handy to have on hand during a consultation, such as a web address or phone number. This information will always be displayed when you visit this page

The content herein is provided for informational purposes and does not replace the need to apply professional clinical judgement when diagnosing or treating any medical condition. A licensed medical practitioner should be consulted for diagnosis and treatment of any and all medical conditions.

Connect

Copyright 2024 Oxbridge Solutions Limited, a subsidiary of OmniaMed Communications Limited. All rights reserved. Any distribution or duplication of the information contained herein is strictly prohibited. Oxbridge Solutions receives funding from advertising but maintains editorial independence.